Turkish Journal of Physical Medicine and Rehabilitation 2017 , Vol 63 , Num 4
A rare case of neuro-Behçet’s disease presenting with limbic encephalitis
Dilcan Kotan 1 ,Sinem Sağ 2 ,Belma Doğan Güngen 3 ,Pınar Polat 3
1 Department of Neurology, Medical Faculty of Sakarya University, Sakarya, Turkey
2 Department of Rheumatology, Sakarya University Training and Research Hospital, Sakarya, Turkey
3 Department of Neurology, Sakarya University Training and Research Hospital, Sakarya, Turkey
DOI : 10.5606/tftrd.2017.480 Behçet's syndrome is a recurrent systemic inflammation with an unknown etiology. The onset of the condition often occurs in the second decade of life and it is more common in males than in females. One of the most feared organ involvements associated with BS is neurological involvement, which often affects the brain stem, although hemispheric involvement may be primary in a limited number of patients. Parenchymal neurological involvement in BS affects the prognosis unfavorably, as it may result in severe sequelae or mortality. Early diagnosis and treatment is important to prevent sequelae. Herein, we report the first case of neuro-Behçet’s disease presenting with limbic encephalitis who received early stage immunotherapy. Keywords : Intravenous immunglobulin; limbic encephalitis; neuro-Behçet’s disease